Abernethy Malformation Type 1b
نویسندگان
چکیده
Teaching point: Extrahepatic portosystemic shunt is a rare congenital condition, associated with other anomalies, for which prompt radiological diagnosis and treatment are important to prevent complications.
منابع مشابه
Abernethy malformation: a case report
BACKGROUND Abernethy malformation is a very rare congenital vascular malformation defined by diversion of portal blood away from liver. It is commonly associated with multiple congenital anomalies. We present a case of Abernethy malformation, without associated congenital anomalies from India. CASE PRESENTATION A 5-year-old female child presented with short history of jaundice. A provisional ...
متن کاملAbernethy malformation with portal vein aneurysm.
We present the case of a 24-year-old man who was incidentally diagnosed with congenital extrahepatic portosystemic shunt with portal vein aneurysm during an investigation for non-specific abdominal pain. These are rare anomalies, and to the best of our knowledge, this is the first case reported with both anomalies associated together. Ultrasound, including color Doppler, computed tomography, an...
متن کاملRecurrent Hyperammonemia After Abernethy Malformation Type 2 Closure: a Case Report.
The Abernethy malformation is a rare congenital malformation defined by the presence of an extrahepatic portosystemic shunt. Although most patients are asymptomatic, clinical encephalopathy is present in 15% of cases. We present a patient with type 2 Abernethy malformation, hyperammonemia, and encephalopathy. Shunt closure was performed successfully using interventional angiography; however, hy...
متن کاملManagement strategy after diagnosis of Abernethy malformation: a case report
INTRODUCTION The Abernethy malformation is a rare anomaly with a widely variable clinical presentation. Many diagnostic dilemmas have been reported. Nowadays, with the evolution of medical imaging, diagnosis can be made more easily, but management of patients with an Abernethy malformation is still open for discussion. CASE PRESENTATION In this case study, we describe a 34-year-old Caucasian ...
متن کاملSingle Stage Endovascular Treatment of a Type 2 Abernethy Malformation: Successful Nonsurgical Outcome in a Case Report
Abernethy malformations are a rare collection of congenital hepatic portosystemic shunts. Our 19-year-old patient is with a type 2 Abernethy malformation elected permanent shunt closure following worsening dyspnea. This report details a single stage endovascular technique wherein shunt closure was achieved immediately by placement of an aortic endograft. At 5-month follow-up, the patient report...
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ژورنال
عنوان ژورنال: Journal of the Belgian Society of Radiology
سال: 2021
ISSN: ['2514-8281']
DOI: https://doi.org/10.5334/jbsr.2431